Elastosis perforans serpiginosa
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| Elastosis perforans serpiginosa | |
|---|---|
| Other names | EPS[1] |
 | |
| Elastosis perforans serpiginosa: Hyperkeratotic plaque of papules[2] | |
Elastosis perforans serpiginosa is a unique perforating disorder characterized by transepidermal elimination of elastic fibers and distinctive clinical lesions, which are serpiginous in distribution and can be associated with specific diseases.[3][4]
![Histopathology of elastosis perforans serpiginosa: Degenerated elastic fibers and transepidermal perforating canals (arrow points at one of them)[2]](https://upload.wikimedia.org/wikipedia/commons/thumb/3/3e/Histopathology_of_elastosis_perforans_serpiginosa.jpg/120px-Histopathology_of_elastosis_perforans_serpiginosa.jpg)
Histopathology of elastosis perforans serpiginosa: Degenerated elastic fibers and transepidermal perforating canals (arrow points at one of them)[2]
This condition is inherited in an autosomal dominant manner.
![Histopathology of elastosis perforans serpiginosa: Degenerated elastic fibers and transepidermal perforating canals (arrow points at one of them)[2]](/wiki/File:Histopathology_of_elastosis_perforans_serpiginosa.jpg)
See also
References
- ↑ "OMIM Entry - 130100 - ELASTOSIS PERFORANS SERPIGINOSA; EPS". omim.org. Retrieved 19 April 2019.
- ↑ 2.0 2.1 Hosen, Mohammad J.; Lamoen, Anouck; De Paepe, Anne; Vanakker, Olivier M. (2012). "Histopathology of Pseudoxanthoma Elasticum and Related Disorders: Histological Hallmarks and Diagnostic Clues". Scientifica. 2012: 1–15. doi:10.6064/2012/598262. ISSN 2090-908X. PMC 3820553. PMID 24278718.
-Creative Commons Attribution 3.0 Unported license - ↑ Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). Page 1041. McGraw-Hill. ISBN 0-07-138076-0.
- ↑ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 978-1-4160-2999-1.
