Erythrokeratodermia with ataxia

From dermwiki
Created
2024-05-05 05:21
Contributors
WikiTeq Adm and Dermwiki
Article status
Unassigned

Clinical

Features

Variants

Images

Differential

Histology

Features

Variants

Images

Differential

Pathophysiology

Epidemiology

Associations

Workup

Labs

Imaging

Diagnostic criteria

Management

Treatment

Monitoring

Counseling

Other considerations

Erythrokeratodermia with ataxia
Other namesGiroux–Barbeau syndrome[1]
Autosomal dominant - en.svg
Erythrokeratodermia with ataxia is inherited in an autosomal dominant fashion.
SpecialtyMedical genetics

Erythrokeratodermia with ataxia is a condition characterized by erythematous, hyperkeratotic plaques with fine, white, attached scales distributed almost symmetrically on the extremities.[1]

See also

References

  1. 1.0 1.1 Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 978-1-4160-2999-1.

External links